Wyniki wyszukiwania - Biblioteka Nauki

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Pterotopteryx dodecadactyla (HUBNER, 1813) (Lepidoptera, Alucitidae) - nowe stanowisko w północno-wschodniej Polsce

100%

Buszko J. , Jurkiewicz E.

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2015

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tom 34

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nr 2

2

Analiza błędów technologicznych analizatorów tarczowych

100%

Jurkiewicz E. , Leśniczak J.

Problemy Techniki Uzbrojenia

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2002

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tom R. 31, z. 85

129--139

PL

W artykule przedstawiono analizę dokładności analizatorów tarczowych stosowanych w głowicach optoelektronicznych pocisków samonaprowadzających się na cel w aspekcie jakości wykonania wzoru tarczy, jej współosiowości z układem optycznym oraz drgań tarczy modulacyjnej.

EN

An analysis of accuracy of disc analysers used in homing missile optic-electronic heads is presented taking into account the vibrations of modulation disc and also the workmanship quality of disc pattern and its adjustment against a system optical axis.

3

Pasożyty jazia (Leuciscus idus (L.)) poławianego w jeziorze Dąbie

80%

Sobecka E. , Jurkiewicz E. , Wawrzonek K.

Wiadomości Parazytologiczne. Suplement

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2004

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tom 50

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Parasite fauna of ide, Leuciscus idus [L.] in Lake Dabie, Poland

80%

Sobecka E. , Jurkiewicz E. , Piasecki W.

Acta Ichthyologica et Piscatoria

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2004

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tom 34

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nr 1

EN

Background. The previous survey on parasites of ide in Poland was carried out in 1987 and there has been no data available on the parasites of this fish from areas in Poland west of the Vistula River. The aim of the present study was to survey the parasite fauna of ide, Leuciscus idus in Lake Dąbie and to compare the. Materials and Methods. Standard parasitological procedures were applied to 110 individuals of ide, Leuciscus idus (L.) caught within 2000-2003 in Lake Dąbie, Szczecin, Poland. Results. All fish examined were infected with parasites. The parasites recovered, represented 32 species and 11 higher taxa (Oligohymenophorea, Myxosporea, Monogenea, Digenea, Nematoda, Palaeacanthocephala, Euacanthocephala, Hirudinea, Copepoda, Branchiura, and Bivalvia). A total of 15 parasite species represented new host records for ide in Poland (Dermocystidium sp. , Myxidium pfeifferi, Zschokella nova, Myxobolus carassii, M. muelleri, Henneguya cutanea, Tripartiella copisa, Paradiplozoon bliccae, Gyrodactylus prostae, Anisakis simplex, Streptocara crassicauda, Philometra rischta, Argulus foliaceus, Piscicola geometra, Hemiclepsis marginata). The highest values of prevalence were recorded for: Ergasilus sieboldi, Diplostomum spp., Tylodephys clavata, and Paracoenogonimus ovatus. Results. with the relevant data on the subject published by other authors. Conclusion. Infection parameters of the presently surveyed ide were distinctly different from those previously described. It is possible that populations of some parasites grew within the past 20 years.

5

Mild Zellweger syndrome due to a novel PEX6 mutation: correlation between clinical phenotype and in silico prediction of variant pathogenicity

61%

Rydzanicz M. , Stradomska T. J. , Jurkiewicz E. , Jamroz E. , Gasperowicz P. , Kostrzewa G. , Ploski R.

Journal of Applied Genetics

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2017

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tom 58

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nr 4

6

Homozygote for mutation c.1204 plus 1G A of the ARSA gene presents with a late-infantile from of metachromatic leukodystrophy and rare MRI white matter lesion type

61%

Lugowska A. , Szymanska K. , Kmiec T. , Tarczynska I. , Czartoryska B. , Tylki-Szymanska A. , Jurkiewicz E.

Journal of Applied Genetics

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2005

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tom 46

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nr 3

337-339

EN

The metachromatic leukodystrophy (MLD) - causing mutation c. 1204 + 1G > A damages an intron-exon splice site recognition sequence. This results in a complete loss of enzymatic activity of arylsulfatase A (ARSA) protein molecules. We have found a late-infantile type MLD-patient to be homozygous for this mutation, which was not reported earlier, but is consistent with previous suggestions. Interestingly, the cerebral magnetic resonance imaging (MRI) in this patient displayed linear or punctuate structures radiating in the demyelinated white matter, which resembled the patterns described in Pelizaeus-Merzbacher disease. It should be emphasised that whenever a cerebral MRI demonstrates the 'tigroid' or 'leopard-skin' demyelination pattern not only Pelizaeus-Merzbacher disease, but also metachromatic leukodystrophy diagnosis should be considered; this suggests the necessity of ARSA activity estimations in patients with such specific MRI patterns.

7

Magnetic resonance imaging of brain abnormalities in patients with the Nijmegen breakage syndrome

61%

Bekiesinska-Figatowska M. , Chrzanowska K. H. , Jurkiewicz E. , Wakulinska A. , Rysiewski H. , Gladkowska-Dura M. , Walecki J.

Acta Neurobiologiae Experimentalis

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2004

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tom 64

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nr 4

8

MRI-monitored cord blood-derived cell transplantation to the ventricular system of child with global cerebral ischemia-a case report

41%

Janowski M. , Kmiec T. , Jurkiewicz E. , Kropiwnicki T. , Habich A. , Kotulska K. , Jelonek E. , Sarnowska A. , Litwin M. , Boruczkowski D. , Lukomska B. , Walecki J. , Roszkowski M. , Jozwiak S. , Domanska-Janik K.

Acta Neurobiologiae Experimentalis

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2011

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tom 71

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nr 1

EN

Introduction: Neurological disorders are the most common cause of serious disability and have a major impact on financial healthrelated burden to society. Most of them are definitely associated with cell death: sudden or chronic. Conventional treatment methods yield disappointing results. Thus the discoveries in stem cell biology have fueled the interest in cell-based therapeutical approach. Based on experimental data cord blood has been proposed as a novel, autologous cell source for pediatric population. Non-invasive monitoring of cell fate following transplantation has been recently recommended as a basis for rational stem cell therapy. Subject: One year old child experienced devastating, cardiac arrest-induced cerebral ischemia. Despite a broad rehabilitation program diagnose of vegetative state has been established three months later. After next three months of continued rehabilitation no noticeable improvement has also been found and the child has been included into study. The protocol has been approved by the ethical commission of The Children’s Memorial Health Institute in Warsaw, Poland. Then the child’s own cord blood cells have been neurally-converted over 10 days in culture within GMP facility. Prior to transplantation cells were labeled with iron oxide (SPIO) for MR imaging. For scaling sensitivity of MR signal different concentrations of SPIO-labeled cells were scanned in the phantom. Then patient received monthly 3 subsequent cell infusions (1.2 x 107 cells each) to lateral ventricles. The follow up continued up to 6 months and included both clinical assessment and MR examinations. Results: High efficiency of neural cell conversion and SPIO labeling as well as no cytotoxicity were observed. The employed method of cell transplantation was found to be efficient to deliver cells to CNS as confirmed by MR imaging. Gradual decrease of SPIO signal intensity was observed over the period of follow up. No adverse events or abnormal reaction to cell implantation was detected. The follow up revealed mild functional improvement - decreased nystagmus, spasticity and the number of epileptic seizures. Moreover, the features of the child contact with parents has appeared, thus vegetative state can not be diagnosed any more. Conclusions: This report indicates that transplantation of autologous, neurally-committed cord blood-derived cells to the ventricular system of child is safe, feasible and able to result with mild functional improvement. Additionally cell-related MRI signal can be monitored for more than 4 months in transplanted brain hemisphere. Supported by MSHE grants no 0141/B/P01/2008/35 and 0142/B/ P01/2008/35.