Results of Surgical and Postoperative Treatment of Syndactyly in Epidermolysis Bullosa

• Autorzy: Bartłomiej Noszczyk , Joanna Jutkiewicz , Józef Jethon , Mirosław Wróbel , Piotr Szopiński
• Języki publikacji: EN

Abstrakty

EN

Use of small autologous skin grafts or leaving the defects and waiting for their spontaneous reepidermization are one of the methods of wound management after surgical treatment of hand contractures in Epidermolysis bullosa. This techniques are believed to allow quick wound healing, however this does not seem universally possible.The aim of the study was to assess healing rate and incidence of early recurrence after using of both techniques.Material and methods. Eleven operations of hand contracture were performed, including two recurrent cases after previous surgeries. Skin grafts were used in eight cases. Kirshner wires were not used and the fingers were stabilized in an extended position only with a supportive dressing. In the early postoperative period, dressings were made in the operation room and patients were admitted for 24-hour hospitalizations no more than once a week.Results. Complete healing before day 35 was achieved only in five cases. In the remaining cases, dressings in the operating room were abandoned between day 35 and 40 and the patients were referred to further treatment in the outpatient setting. Outpatient dressings were done without anesthesia which in the event of unhealed spaces between the fingers, seemed to impair their separation and facilitate early recurrences of syndactyly. Two cases of early recurrence (18%), during the first year after the operation, were noted in one patientConclusions. Our results indicate that the postoperative wound healing does not depend on the use of skin grafts and can be much longer than some previous studies suggested. This shortens the period of full efficiency between the recurrences. Clinical observations also indicate that this affects the risk of early recurrences. Despite that, their number is similar to the value considered good in the literature.

Słowa kluczowe

EN

dystrophic epidermolysis bullosa; hand surgery; pseudosyndactyly; hand contractures; scaring; deformities; skin grafts; poor healing; dressings; recurrence

• Wydawca: Index Copernicus International
• Czasopismo: Polish Journal of Surgery
• Rocznik: 2008
• Tom: 80
• Numer: 8
• Strony: 394-403

Daty

wydano

2008-08-01

online

2008-09-10

Twórcy

autor

Bartłomiej Noszczyk

• Department of Plastic Surgery, Medical Centre of Postgraduate Education, Warsaw

autor

Joanna Jutkiewicz

• Department of Pediatric Surgery, Prof. Bogdanowicz Memorial Hospital, Warsaw

autor

Józef Jethon

• Department of Plastic Surgery, Medical Centre of Postgraduate Education, Warsaw

autor

Mirosław Wróbel

• Department of Pediatric Surgery, Prof. Bogdanowicz Memorial Hospital, Warsaw

autor

Piotr Szopiński

• Department of General and Vascular Surgery, Medical University, Warsaw

Bibliografia

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Identyfikatory

DOI

10.2478/v10035-008-0056-8