Recurrence of retroperitoneal fibrosis with pancreatic involvement - the importance of imaging methods

• Autorzy: Regina Djerassi , Martin Krupev , Milena Nikolova , Nikolai Naumov , Valeri Marianovski , Chavdar Elenkov , Arman Postadjian
• Języki publikacji: EN

Abstrakty

EN

Retroperitoneal fibrosis (RPF) is a rare disease associated with the development of chronic inflammation and fibrogenesis in the retroperitoneal space. The disease usually manifests with acute or acute over chronic renal failure and/or urosepsis. Pancreatic involvement in RPF is rare but has been described in the literature. The diagnosis of RPF is made mainly by imaging methods. Abdominal echography scan reveals the presence of an obstruction with or without inflammation; computed tomography and magnetic resonance imaging show the type and the spreading of fibrosis. Here, we report a 50-year-old female patient diagnosed with RPF during operative intervention in 2003. Initial treatment with corticosteroids and tamoxifen lead to remission. In 2007, late recurrence was observed, with tumor-like lesions over the upper, posterior, and anterior surfaces of the pancreas, spreading to intraperitoneal structures and more pronounced on the left side. Abdominal echography on day 30 showed that corticosteroid treatment lead to a decrease in the tumor-like lesions.

Słowa kluczowe

EN

Retroperitoneal fibrosis; Pancreatic involvement; Diagnosis; Treatment; Corticosteroids; Azathioprine; Ureteral desobstruction

• Czasopismo: Open Medicine
• Rocznik: 2008
• Tom: 3
• Numer: 3
• Strony: 365-369

Daty

wydano

2008-09-01

online

2008-07-10

Twórcy

autor

Regina Djerassi

• Clinic of Nephrology, University Hospital Alexandrovska, Sofia, Bulgaria,

autor

Martin Krupev

• Department of Radiology, University Hospital Alexandrovska, Sofia, Bulgaria

autor

Milena Nikolova

• Clinic of Nephrology, University Hospital Alexandrovska, Sofia, Bulgaria

autor

Nikolai Naumov

• Emergency Hospital Pirogov, Sofia, Bulgaria

autor

Valeri Marianovski

• Emergency Hospital Pirogov, Sofia, Bulgaria

autor

Chavdar Elenkov

• Department of Urology, University Hospital Alexandrovska, Sofia, Bulgaria

autor

Arman Postadjian

• Department of Cardiology, University Hospital St. Anna, Sofia, Bulgaria

Bibliografia

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Identyfikatory

DOI

10.2478/s11536-008-0017-y